What is Jervell and Lange-Nielsen Syndrome?

Jervell and Lange Nielsen syndrome (JLNS) is a rare cardio-auditory disorder with an autosomal recessive pattern of inheritance. JLNS was first reported in Norway in 1957. Bilateral sensorineural hearing loss, a prolonged QTc interval, and a high risk of sudden cardiac death are some characteristic features of JLNS. It's a type of long QT syndrome (LQTS) passed down through the generations.